Introduction
Sinus venosus atrial septal defects (SVASDs), originally described in
1858, account for approximately 4%-11% of all atrial septal defects
(ASDs)[1,2].
The typical SVASD is an interatrial communication that results from a
deficiency of the common wall between the superior vena cava (SVC) and
the right-sided pulmonary veins[2,3].
SVASD is commonly associated with anomalous pulmonary venous connections
(APVCs) involving some or all of the pulmonary veins[3,4],
which produces additional left-to-right shunting. The basic principle of
repair is redirection of the APVC through the interatrial communication
into the left atrium.
In contrast to operative repair of secundum ASD, the surgical approach
for SVASD is more complex and carries the risk of stenosis of the SVC or
pulmonary veins, residual shunting, and sinus node dysfunction[4].
We reviewed outcomes for patients who underwent SVASD repair at
Bhanubhai and Madhuben Patel Cardiac Centre, Karamsad, Anand, Gujarat,
India, with a focus on patient survival and development of arrythmias.